Autosomal dominant
Mc hereditary bleeding disordr
Platlet adhesion defect
Prolonged bt,aptt
Decrease factor 8 may b mod reduced
3 types
Type 1-- partial redctn in vwf
Typ 2-- abnorml form vwf
Typ3-- total lack vwf
defctv platlet aggregation with ristocetin
Rx factor 8 cryoppt
Additional fact ::hemarthrosis
N muscle hematoma z rare
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